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fibrolipomatous hamartoma

Friday 28 May 2010

Predisposition

- tuberous sclerosis

  • Tuberous sclerosis is a rare congenital disorder with an incidence of 1 in 6000 births.
  • The classic triad is seizure, mental deficiency, and angiofibromas.
  • Orofacial manifestations include fibrous hyperplasia, hemangioma, bifid uvula, cleft lip and palate, macroglossia, high arched palate, and enamel defects.
  • Benign tumors of the jaws including desmoplastic fibroma, calcifying odontogenic tumor, and odontogenic myxoma have been recently reported in tuberous sclerosis.

References

- Fibrolipomatous hamartoma in a patient with tuberous sclerosis: report of a case. Celenk P, Alkan A, Canger EM, G├╝nhan O. Oral Surg Oral Med Oral Pathol Oral Radiol Endod. 2005 Feb;99(2):202-6. PMID: 15660093