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intracranial rhabdomyosarcoma

Wednesday 11 January 2012

Tumors of the central nervous system (CNS) composed of pure mesenchymal derivatives with both embryonal and mature striated muscle cells devoid of neuroblastic elements should be considered rhabdomyosarcomas.

Some 17 cases have been reported (1985).

Localization

- temporal lobes
- cerebellar vermis

Types

- intracranial embryonal rhabdomyosarcoma
- intracranial alveolar rhabdomyosarcoma

See also

- parameningeal rhabdomyosarcoma

References

- Successful treatment of a child with a primary intracranial rhabdomyosarcoma with chemotherapy and radiation therapy. Guilcher GM, Hendson G, Goddard K, Steinbok P, Bond M. J Neurooncol. 2008 Jan;86(1):79-82. PMID: 17579809

- Primary rhabdomyosarcoma of brain and cerebellum. Report of four cases in infants: an immunohistochemical study. Taratuto AL, Molina HA, Diez B, ZĂșccaro G, Monges J. Acta Neuropathol. 1985;66(2):98-104. PMID: 4013672

- Seiz M, Radek M, Buslei R, Kreutzer J, Hofmann B, Kottler U, Doerfler A, Nimsky C, Fahlbusch R. Alveolar rhabdomyosarcoma of the clivus with intrasellar expansion: Case report. Zentralbl Neurochir. 2006 Nov;67(4):219-22. PMID: 17139605