Home > D. Systemic pathology > Genetic and developmental anomalies > generalized peeling skin syndrome

generalized peeling skin syndrome

Monday 6 February 2012

Definition: Generalized peeling skin syndrome (PSS) is an autosomal recessive genodermatosis characterized by lifelong, continuous shedding of the upper epidermis.

Etiology

- mutation in the CHST8 gene in autosomal recessive peeling skin syndrome. (#22289416#)