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congenital polycystic tumor of the atrioventricular node

Friday 13 January 2006

Congenital polycystic tumor of the atrioventricular node is a rare tumor of disputed histogenesis. It constant location in the atrioventricular node separates it from other cardiac cysts and tumors of indisputable endodermal origin.

Morphologic and histochemical features of the tumor fail to conclusively favor either a mesothelial or an endodermal genesis.

References

- Polycystic tumor of the atrioventricular nodal region in a man with Emery-Dreifuss muscular dystrophy. Strøm EH, Skjørten F, Stokke ES. Pathol Res Pract. 1993 Sep;189(8):960-4; discussion 965-7. PMID: #8302717#

- Congenital polycystic tumor of the atrioventricular node. Autopsy study with immunohistochemical findings suggesting endodermal derivation.
Duray PH, Mark EJ, Barwick KW, Madri JA, Strom RL. Arch Pathol Lab Med. 1985 Jan;109(1):30-4. PMID: #2578779#

- Travers H. Congenital polycystic tumor of the atrioventricular node: possible familial occurrence and critical review of reported cases with special emphasis on histogenesis. Hum Pathol. 1982 Jan;13(1):25-35. PMID: #7076192#

- De subitaneis mortibus. XXVI. Fatal electrical instabiltiy of the heart associated with benign congenital polycystic tumor of the atrioventricular node. James TN, Galakhov I. Circulation. 1977 Oct;56(4 Pt 1):667-78. PMID: #902393#