Lung in Hurler disease; lung involvement in Hurler disease, Alpha-L-Iduronidase Deficiency, IDUA Deficiency, MPS I. Includes: Hurler Syndrome (MPS I H), Hurler-Scheie Syndrome (MPS I H/S), Scheie Syndrome (MPS I S)
Digital case
Case 202 (HPC:202) : Lung in Hurler disease
Synopsis
interstitial pneumonia
interstitial deposition of mucopolysaccharides
cholesterol bronchiolitis
See also
Hurler disease
References
NCBI (...)
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Disease localization
Localization of a disease. The localization is described by an adjective.
Articles
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pulmonary Hurler disease
14 March 2011 -
desmin cardiomyopathy
28 August 2007Synopsis
diffuse myocyte hypertrophy
nuclear pleomorphism without intramyocardial fibrosis
myofibers distorted by intracytoplasmic, pale, waxy hyaline inclusions
conduction fibers grossly swollen and preferentially involved
trichrome stain pale pink inclusions against a red background
inclusions PAS negative and not congophilic
Immunochemistry
desmin immunohistochemical staining variable dense staining of inclusions in some areas faint to no staining
Electron microscopy (...) -
adenoviral hepatitis
13 April 2004adenovirus hepatitis
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renal trichosporonosis
30 January 2006See also
fungi Trichosporon asahii
fungal infections fungal systemic infections systemic trichosporonosis -
EBV hepatitis
6 April 2004Epstein-Barr viral hepatitis
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peritoneal endometriosis
12 March 2007subserous endometriosis
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hepatic glycogen storage diseases
24 July 2007hepatic GSDs, hepatic glycogenoses
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digestive infantile myofibromatosis
22 March 2007Localization
intestinal infantile myofibromatosis
See also
infantile myofibromatosis -
hepatic Meckel syndrome
9 November 2006hepatic lesions in Meckel syndrome
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adrenal Wolman disease
10 November 2004Synopsis
adrenal storage disease
adrenal calcifications
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