PSPPT; solid-pseudopapillary tumor of the pancreas, Frantz tumor, Frantz’s tumor; solid pseudopapillary tumor of the pancreas; ICD-O codes Solid pseudopapillary neoplasm 8452/1, Solid pseudopapillary carcinoma 8452/3; pancreatic solid pseudopapillary tumor; pancreatic solid and pseudopapillary tumor; Solid-pseudopapillary neoplasm of the pancreas PathConsult
Definition: Solid pseudopapillary neoplasms of the pancreas are rare pancreatic tumors with mostly benign behavior, affecting (...)
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Translocation-associated tumors
Articles
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pancreatic solid pseudopapillary tumor
12 November 2003 -
clear cell sarcoma of the kidney
14 July 2004, by JACCSK, renal clear cell sarcoma; bone-metastasizing renal tumour of childhood AGCOH PathConsult eMedicine
Digital slides
Case 66 (HPC:66) : Clear cell sarcoma of the kidney (CCSK)
Definition: Clear cell sarcoma of the kidney (CCSK) is a malignant renal tumor of childhood with a propensity to metastasize to bone and other organs. CCSK is linked to internal tandem duplications (ITDs) of the BCOR gene.
This tumor may also recur many years after its initial diagnosis. The average age (...) -
myxoid/round cell liposarcoma
7 October 2005myxoid liposarcoma and round cell liposarcoma group; MRC-LPS
Definition: Myxoid and round cell liposarcoma accounts for about 30% to 35% of all liposarcomas and, even if still classified by the World Health Organization (WHO) as 2 distinct subtypes, share both clinical and morphologic features.
See also :
myxoid liposarcoma
round cell liposarcoma
Lesions combining both patterns are frequent and wide agreement exists in considering round cell liposarcoma as the high grade counterpart (...) -
myxoid liposarcoma
1 November 2007PO
Definition: Myxoid liposarcoma displays variably aggressive behavior and responds poorly to available systemic therapies.
Images
myxoid liposarcoma https://twitter.com/histiocytosisX/status/748157284644196352 https://twitter.com/a_sleeping_dog/status/773402045911007232 https://twitter.com/JMGardnerMD/status/737075990086590466 https://twitter.com/DanglisFotiosMD/status/734976870110900225 https://twitter.com/solcosao/status/706608037868404736
FISH FUS rearrangement (...) -
TFE3-associated renal cell carcinoma
18 September 2003TFE3 gene fusions associated renal cell carcinoma, pediatric renal cell carcinomas with Xp11.2 rearrangements; Xp11 Translocation Renal Cell Carcinoma (RCC); xp11 translocation renal cell carcinomas
Definition: The renal cell carcinomas (RCCs) associated with Xp11.2 translocations (TFE3 transcription factor gene fusions) are rare tumors predominantly reported in children.
Images
TFE3-associated renal cell carcinoma
https://twitter.com/yasminelys/status/800834875699892224 (...) -
alveolar rhabdomyosarcoma
25 November 2003Images
Alveolar rhabdomyosarcoma.
https://twitter.com/histiocytosisX/status/699599913013923840
https://twitter.com/seattlequinns/status/855202143564742656
ARMS : focal desmin w/ diffuse myogenin in A-RMS (PCR + PAX3-FOXO1)
https://twitter.com/histiocytosisX/status/730475540524699649
Compact ARMS : Alveolar rhabdomyosarcoma may lack alveolar spaces. Solid nodules uniform round cells,fibrous septa. DIFFUSE myogenin.
https://twitter.com/JMGardnerMD/status/856870953011347456 (...) -
lipoblastoma
7 October 2005Fetal Lipoma, Infantile Lipoma, Embryonic Lipoma
Definition: Lipoblastoma is a rare benign tumor that arises from embryonic adipose tissue and usually occurs in young children. It is a lobulated, localized (lipoblastoma) or diffuse (lipoblastomatosis) tumor, resembling fetal adipose tissue.
Images
Lipoblastoma
https://twitter.com/DrBastaki/status/767703201810374656
https://twitter.com/kabeerkshah/status/711948424606670849
https://twitter.com/GSomersPath/status/875061142745436161 (...) -
aggressive angiomyxoma
7 February 2006AAMs, ’aggressive’ angiomyxoma; deep aggressive angiomyxoma
Definition: Aggressive angiomyxoma (AA) is a distinctive, locally aggressive, fibromyxoid tumor of the pelvic and genital soft tissues.
Digital case
JRC:1443 : Aggresive angiomyxoma of pelvic soft tissues.
JRC:14570 : Aggresive angiomyxoma of peritoneum (ischiorectal fossa).
Images
Deep (agressive) angiomyxoma. Young women vulvar tumor
https://twitter.com/luishcruzc/status/758685476341415936 (...) -
giant cell angiofibroma
11 October 2005Definition: Giant cell angiofibroma is a phenotypic variant of solitary fibrous tumor (SFT).
Giant cell angiofibroma seems most often to arise in the head and neck region (predominantly orbit) of adults and which, with the passage of time.
It may well prove to be a variant of solitary fibrous tumour characterized by prominent multinucleate giant cells and lipofibromatosis.
It is a rare tumour occurring predominantly in the hands or feet of infants and young children.
it shows a high (...) -
angiomatoid fibrous histiocytoma
14 October 2003Definition: Angiomatoid fibrous histiocytoma (AFH) is a rare soft tissue tumor of low malignant potential and uncertain differentiation.
Images
https://twitter.com/JMGardnerMD/status/735824693718974464
https://twitter.com/LizMontgomeryMD/status/1123321496837996544
https://twitter.com/histiocytosisX/status/883309952303079429
https://twitter.com/histiocytosisX/status/865226837093384194
https://twitter.com/histiocytosisX/status/753620834925805568 (...)