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pulmonary cystic fibrohistiocytic tumor

Friday 10 January 2014

Cystic fibrohistiocytic tumor of the lung

Cystic fibrohistiocytic tumor of the lung is a rare neoplasm. In many cases it represents a metastasis from a benign or low-grade fibrohistiocytic tumor of the skin, but occasionally it may be primary.

Radiologically it usually occurs as a cystic change of multiple pulmonary nodules, and pneumothorax is the most frequent presenting symptom.

The differential diagnosis includes Langerhans cell histiocytosis, lymphangioleiomyomatosis, pleuropulmonary blastoma, and metastatic endometrial stromal sarcoma.

This disease usually occurs with multiple pulmonary cysts and cavitation.

Open references

- Cystic fibrohistiocytic tumor of the lung presenting as a solitary lesion. Paci M, Cavazza A, Annessi V, Ricchetti T, Rapicetta C, Sgarbi G. Rare Tumors. 2010 Mar 31;2(1):e14. doi : 10.4081/rt.2010.e14 PMID: 21139943 [Free]