thrombotic microangiopathies, Moschkowitz syndrome, TMA
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thrombotic microangiopathy
15 April 2005 -
dermatitis herpetiformis
29 June 2004herpetiform dermatitis
Definition: Dermatitis herpetiformis is characterized by papules, vesicles, and occasional bullae on an erythematous, often urticarial base.
Dermatitis herpetiformis is associated with gluten-sensitive enteropathy. It causes small pruritic vesicles.
Histologically it shows papillary neutrophilic microabscesses and a mixed dermal inflammatory infiltrate. DIF shows a granular pattern of IgA in the dermal papillae.
Digital cases
UI:924 - Dermatitis herpetiformis (...) -
Niemann-Pick disease type C
30 May 2003Niemann-Pick disease type C, NPC
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campomelic dysplasia
14 January 2005campomelic dysostosis, camptomelic dysplasia, camptomelic syndrome, campomelic dwarfism
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pentalogy of Cantrell
19 December 2005THAS, TAS, thoracoabdominal syndrome, Cantrell syndrome, "shagreen skin" pentalogy
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Kostmann disease
21 September 2007SCN3, severe congenital neutropenia type 3, autosomal recessive severe congenital neutropenia
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lichen striatus
17 June 2004Images
Lichen striatus (lichenoid inflammation and perieccrine inflammation ) https://twitter.com/faisalmohammedi/status/834896649977802754 https://twitter.com/GBRainwater/status/854350881856344067
Synopsis
lichenoid inflammation
peri-eccrine inflammation / peri-eccrine lymphocytic infiltrate
DIFFERENTIAL:
linear lichen planus
lichen niditus
inflammatory linear verrucous epidermal (...) -
osteogenesis imperfecta
26 May 2004Autosomal dominant disease.
Synopsis
systemic anomalies
perinatal death
premature birth
nonimmune hydrops
low birth weight
ocular anomalies
blue sclerae
craniofacial anomalies
beaked nose
large fontanelles
platyspondyly
skeletal anomalies
short limb dwarfism
beaded ribs
numerous multiple fractures present at birth
soft calvaria
absent calvarial mineralization
hips usually flexed and abducted (frog-leg position)
flattened acetabulae and iliac wings (...) -
cutaneous allograft rejection
26 April 2004References
Bejarano PA, Levi D, Nassiri M, Vincek V, Garcia M, Weppler D, Selvaggi G, Kato T, Tzakis A. The Pathology of Full-thickness Cadaver Skin Transplant for Large Abdominal Defects: A Proposed Grading System for Skin Allograft Acute Rejection. Am J Surg Pathol. 2004 May;28(5):670-675. PMID: #15105657# -
lichen planus
16 June 2004WKP
Definition: Lichen planus is a papulosquamous disease. In its classical presentation, it is characterized by pruritic violaceous papules most commonly on the extremities of middle-aged adults. It may or may not be accompanied by oral and genital mucous membrane involvement. Its course is generally self-limited for a period of several months to years, but it may last indefinitely.
There are many clinical variants described, ranging from lichenoid drug eruptions to association with (...)