Definition : Primary adrenal leiomyosarcoma is a exceedingly rare adrenal tumor thought to be originated from smooth muscle wall of central adrenal vein. SMA and desmin IHC is diffusely positive.
Differential diagnosis
sarcomatoid adrenal cortical carcinoma
malignant PEComa
dedifferentiated liposarcoma
adrenal metastasis
Images
primary adrenal leiomyosarcoma https://twitter.com/BinXu16/status/972093934712344576
See also
adrenal tumors
leiomyosarcoma / (...)
Home > E. Pathology by systems > Endocrine system > Adrenals
Adrenals
-
adrenal leiomyosarcoma
18 March 2018 -
spironolactone bodies
21 September 2016spironolactone body
Images
Conn syndrome: aldosterone secreting adrenal cortical adenoma with spironolactone bodies https://twitter.com/AssaadAM/status/715046004542869504 https://twitter.com/JMGardnerMD/status/828604771506515969
See also
spironolactone
bodies -
Conn syndrome
21 September 2016Images
Conn syndrome: aldosterone secreting adrenal cortical adenoma, note spironolactone bodies https://twitter.com/AssaadAM/status/715046004542869504
See also
clinical syndromes -
adrenal myelolipoma
16 March 2016Images
Adrenal myelolipoma https://twitter.com/baytekinhf/status/709758917446864898 https://twitter.com/Nathan_E_Lee/status/725914805098274816 https://twitter.com/NJanakiMD/status/723315027214737408 https://twitter.com/JMGardnerMD/status/854334231446781955
See also
adrenal tumors
myelolipoma -
malignant pheochromocytoma
6 February 2013adrenal malignant paraganglioma
Digital case
Case 331 (HPC:153) : Peritoneum (adrenal) malignant paraganglioma with lymph node metastases.
Malignant pheochromocytomas/paragangliomas are rare tumors with a poor prognosis. Malignancy is diagnosed by the development of metastases as evidenced by recurrences in sites normally devoid of chromaffin tissue.
Histopathological, biochemical, molecular and genetic markers offer only information on potential risk of metastatic spread. Large size, (...) -
Weiss scoring system
10 August 2012Weiss System; Weiss grading system
References
Adrenocortical Tumors: Improving the Practice of the Weiss System Through Virtual Microscopy: A National Program of the French Network INCa-COMETE. Tissier F, Aubert S, Leteurtre E, Al Ghuzlan A, Patey M, Decaussin M, Doucet L, Gobet F, Hoang C, Mazerolles C, Monges G, Renaudin K, Sturm N, Trouette H, Vacher-Lavenu MC, Viallon V, Baudin E, Bertagna X, Coste J, Libe R. Am J Surg Pathol. 2012 Aug;36(8):1194-1201. PMID: (...) -
cystic neuroblastoma
9 July 2012Digital slide
JRC:4205 : Adrenal cystic neuroblastoma.
Variants
bilateral cystic neuroblastoma
See also
neuroblastomas -
adrenal granulosa theca tumor
21 April 2012Adrenal gland Granulosa, Theca tumor; Theca granulosa cell tumor arising in adrenal
Digital case
JRC:18776 : Adrenal granulosa theca tumor (F, 52 y/o)
See also
adrenal tumors
granulosa cell tumors
References
Theca granuloma cell tumor arising in adrenal. Orselli RC, Bassler TJ. Cancer. 1973 Feb;31(2):474-7. PMID: #4687888# -
adrenal metastasis of a malignant melanoma
16 April 2012Digital case
JRC:14614 : Metastatic malignant melanoma (vs primary CNS-type melanoma vs malignant epithelioid schwannoma) -
atypical adrenal cortical adenoma
16 April 2012Digital case
JRC:14612 : Atypical adrenal cortical adenoma
See also
adrenal cortical adenoma